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>> DESPITE EXTRAORDINARY ADVANCES IN CARE AND STEADILY
IMPROVING OUTCOMES, SOME PATIENTS WITH A SINGLE
VENTRICLE WILL EVENTUALLY EXPERIENCE HEART FAILURE
AND REQUIRE TRANSPLANTATION.
>> THE HEART TRANSPLANT PROGRAM AT CHOP IS A PROGRAM
THAT'S BEEN IN PLACE NOW FOR OVER 20 YEARS.
PATIENTS ARE SEEN INITIALLY IN OUR HEART FAILURE
CARDIOMYOPATHY PROGRAM AS A GROUP THAT WORKS
SPECIFICALLY ON DEALING WITH HEART MUSCLE PROBLEMS
AND WORKING ON MEDICATIONS AND TRYING TO OPTIMIZE
MEDICATIONS TO AVOID HEART TRANSPLANT.
HOWEVER, SOMETIMES DESPITE ALL OF OUR EFFORTS,
THERE IS A SUBSET OF PATIENTS WHO FINALLY REACH
A POINT WHERE THE ONLY OPTION REALLY
IS CARDIAC TRANSPLANTATION.
AND THAT IS A VERY GOOD OPTION FOR THESE FAMILIES
AND FOR THESE PATIENTS.
>> AS PATIENTS AWAIT TRANSPLANTATION,
SOME LIKE 2-YEAR-OLD MYZAY WILL NEED
THE CARDIAC CENTER'S EXPERTISE WITH ASSIST
DEVICES TO HELP THE HEART CONTINUE PUMPING.
>> A HEART TRANSPLANT IS THE COMMENCEMENT
OF A NEW JOURNEY.
IT'S A WAY TO TRANSITION FROM CARE IN WHICH
MANAGEMENT HAS BEEN FOCUSED ON SINGLE VENTRICLE
AND ALL THE CIRCULATORY LIMITATIONS OF THAT
TO A POTENTIAL NEW LIFE.